부신백질이영양증 환자의 치과치료를 위한 외래전신마취 -증례 보고-
Ambulatory Anesthesia Management of the Patient with Adrenoleukodystrophy for Dental Treatment -A Case Report-
서광석, 박소연, 신터전, 김현정,
소속 상세정보
서광석 ( Seo Kwang-Suk ) - 서울대학교 치의학대학원 치과마취과학교실
박소연 ( Park So-Yeon ) - 서울대학교 치의학대학원 소아치과학교실
신터전 ( Shin Teo-Jeon ) - 서울대학교 치의학대학원 치과마취과학교실
김현정 ( Kim Hyun-Jung ) - 경상대학교병원 신장내과
KMID : 0980220100100010045
Abstract
Adrenoleukodystrophy (ALD) is a rare X-linked genetic disorder associated with various central nervous system problems and adrenal insufficiency. It is common in childhood and symptoms include loss of previously acquired neurological abilities, seizures, ataxia, Addison’s disease as well as degeneration of visual and auditory function. These children frequently require anesthesia during imagining procedure such as MRI or during some surgical procedures like gastrostomy. There is special need for careful management because of numerous anesthetic challenges like difficulty in cooperation, seizure disorders, life-threatening airway obstruction, copious oral secretion and possibility of aspiration. In addition, adrenal involvement and hypofunction must be considered for safe anesthesia management. We report a successful anesthetic management in a patient with ALD for dental procedures.
키워드
Adrenoleukodystrophy (ALD) Dental treatment; General Anesthesia; Cooperation difficulty
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