Dental management of Lowe syndrome under general anesthesia in a child: A case report
이소피아, 송지수, 신터전, 김영재, 김정욱, 장기택, 이상훈, 현홍근,
소속 상세정보
이소피아 ( Rhee Sophia ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
송지수 ( Song Ji-Soo ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
신터전 ( Shin Teo-Jeon ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김영재 ( Kim Young-Jae ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김정욱 ( Kim Jung-Wook ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
장기택 ( Jang Ki-Taeg ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
이상훈 ( Lee Sang-Hoon ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
현홍근 ( Hyun Hong-Keun ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
KMID : 1144020190150020173
Abstract
Lowe syndrome, also known as oculocerebrorenal syndrome, is a rare X-linked recessive disorder characterized by a combination of abnormalities associated with ocular (congenital cataracts), nervous system (mental impairment and hypotonia), and renal dysfunction. Dental crowding, over-retained primary teeth, ectopic and delayed eruption of permanent dentition, and taurodontism have been reported as oral findings. Dental care for young patients with Lowe syndrome is complicated by difficulties in behavior management and other systemic conditions of these patients. General anesthesia may be an appropriate and effective option to eliminate the need for repeated visits to the hospital and to provide improved treatment quality for the patient. However, this approach should be used with caution because general anesthesia may induce malignant hyperthermia and metabolic acidosis in patients with Lowe syndrome. This case study reports the dental management of Lowe syndrome in a 4-yearold male patient who presented with multiple caries in his primary dentition under general anesthesia.
키워드
Lowe syndrome; Dental treatment; General anesthesia
원문 및 링크아웃 정보
등재저널 정보